Abstract

Case Report

Resolved complete atrioventricular block and left ventricular severe dysfunction in patient with Wegener’s granulomatis after cyclophosphamide and corticosteroid treatment

Duc Dang*, Lory Trevisan, Jérôme Bouet and Jérôme Taieb

Published: 25 November, 2019 | Volume 4 - Issue 3 | Pages: 216-218

Wegener’s granulomatosis is a systemic granulomatous focus on small to medium sized vessels. It typically affects sinuses, lungs and kidneys due to necrotizing granulomatous vasculitis. Less commonly, cardiac involvement is reported up to 8%-44% of cases [1-3]. It often rises to supraventricular arrhythmia, left ventricular systolic dysfunction, pericarditis, myocarditis, and valvulitis [4,5].

Cardiac conducting tissue involvement is rare and associated with increased mortality. It was only reported in fourteen previous cases, some of them were reversible to medical treatment [6]. 

Read Full Article HTML DOI: 10.29328/journal.jccm.1001071 Cite this Article Read Full Article PDF

Keywords:

Duc Dang, Lory Trevisan, Jérôme Bouet ,Jérôme Taieb

References

  1. Grant SC, Levy RD, Venning MC, Ward C, Brooks NH. Wegener’s granulomatosis and the heart. Br Heart J. 1994;71: 82‑ PubMed: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC483617/
  2. Goodfield NE, Bhandari S, Plant WD, Morley-Davies A, Sutherland GR. Cardiac involvement in Wegener’s granulomatosis. Br Heart J. 1995; 73: 110‑ PubMed: https://www.ncbi.nlm.nih.gov/pubmed/7696016
  3. Pinching AJ, Lockwood CM, Pussell BA, Rees AJ, Sweny P, Evans DJ, et al. Wegener’s granulomatosis: observations on 18 patients with severe renal disease. Q J Med. 1983; 52: 435‑ PubMed: https://www.ncbi.nlm.nih.gov/pubmed/6657912
  4. Forstot JZ, Overlie PA, Neufeld GK, Harmon CE, Forstot SL. Cardiac complications of Wegener granulomatosis: a case report of complete heart block and review of the literature. Semin Arthritis Rheum. 1980; 10: 148‑ PubMed: https://www.ncbi.nlm.nih.gov/pubmed/7292019
  5. Oliveira GHM, Seward JB, Tsang TSM, Specks U. Echocardiographic findings in patients with Wegener granulomatosis. Mayo Clin Proc. 2005; 80: 1435‑ PubMed: https://www.ncbi.nlm.nih.gov/pubmed/16295023
  6. Cassidy CJ, Sowden E, Brockbank J, Teh LS, Ho E. A patient with Wegener’s granulomatosis in apparent remission presenting with complete atrioventricular block. J Cardiol Cases. 2011; 3: e71‑ PubMed: https://www.ncbi.nlm.nih.gov/pubmed/30532841
  7. Wilcke JTR, Nielsen PK, Jacobsen TN. Reversible complete heart block due to Wegener’s granulomatosis. Int J Cardiol. 2003; 89: 297‑ PubMed: https://www.ncbi.nlm.nih.gov/pubmed/12767556
  8. Ruisi M, Ruisi P, Finkielstein D. Cardiac manifestations of Wegener’s granulomatosis: Case report and review of the literature. J Cardiol Cases. 2010; 2: e99‑ PubMed: https://www.ncbi.nlm.nih.gov/pubmed/30524597
  9. Strizhakov LA, Krivosheev OG, Kogan EA, Fedorov DN, Semenkova EN, et al. [Aortal regurgitation and atrioventricular block III in Wegener’s granulomatosis]. Klin Med (Mosk). 2007; 85: 68‑ PubMed: https://www.ncbi.nlm.nih.gov/pubmed/18318172

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